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DeCS
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Descriptor English:
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Hemoglobinuria, Paroxysmal
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Descriptor Spanish:
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Hemoglobinuria Paroxística
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Descriptor Portuguese:
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Hemoglobinúria Paroxística
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Synonyms English:
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Marchiafava-Micheli Syndrome
Paroxysmal Hemoglobinuria
Paroxysmal Hemoglobinuria, Cold
Paroxysmal Hemoglobinuria, Nocturnal
Cold Paroxysmal Hemoglobinuria
Hemoglobinuria, Cold Paroxysmal
Hemoglobinuria, Nocturnal Paroxysmal
Hemoglobinuria, Paroxysmal Cold
Hemoglobinuria, Paroxysmal Nocturnal
Marchiafava Micheli Syndrome
Nocturnal Paroxysmal Hemoglobinuria
Syndrome, Marchiafava-Micheli
Paroxysmal Cold Hemoglobinuria
Paroxysmal Nocturnal Hemoglobinuria
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Tree Number:
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C15.378.071.141.560
C15.378.190.625.460
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Definition English:
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A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. |
History Note English:
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78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
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Allowable Qualifiers English:
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Record Number:
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6607
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Unique Identifier:
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D006457
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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